oxygenin,1389
phosphodiesteraseinhibitorsin,1390
prostanoidsin,1389
subcutaneousprostacyclinanaloguesin,1389
inpregnancy,1446–1447
inprematurity,205–207
acute,205
causesof,205t
diagnosisof,205
echocardiographyfor,205
treatmentof,205–207
pulmonaryvasculardisease
incongenitalheartdisease,1381
inunrepairedcongenitalheartdisease,1381–1383,1383f
pulmonaryvenoocclusivediseaseand,1386
inshuntlesions,1523–1524,1524f
transpositionofthegreatarteriesand,122
surgicalmanagementof,689
Pulmonaryoutflowtractobstruction,ventricularseptaldefectand,566–567
Pulmonaryovercirculation,1264f
Pulmonarystenosis,775–802
afterinterventionsfor,802
angiographyin,787
associatedanomalieswith,775
balloondilationin,798–800,799f–800f
cardiaccatheterizationin,787,787f
chestradiographin,782,782f
clinicaldiagnosisof,780–787
computedtomographyin,786
developmentalconsiderationswith,779,780f
echocardiographyin,782–785,782f–784f
electrocardiogramin,781–782
fetalballoonpulmonaryvalvuloplastyin,795–796
hemodynamicsin,787–788
implicationsinadultlife,802
incidenceof,775
interventionalcatheterizationfor,789–795
keydiagnosticfeaturesof,787,787b
magneticresonanceimagingin,786,786f
morphologyandembryologyand,775–779,776f–779f
combinedvalvarandinfundibular,778
infundibularstenosis,778
withothertypesofstenosisoccurringwithintherightventricle,778
ofpulmonaryarterialstenosis,778–779
multipleballoontechniquesfor,796–797,796f
naturalhistoryof,787–788,788f
outcomesofinterventionfor,797–800
physicalexaminationof,781,781t
physiologyof,787–788
presentationof,780–781
recommendationsforlong-termfollowup,800–802
severeorcritical,794–795,795f
severityof,782t
surgicaltherapyfor,788–789,789f
surgicalvalvulotomyin,797–798,798f
therapeuticoptionsfor,788–797
Pulmonarysystem,extracardiacanomaliesof,452
Pulmonarytrunk
anatomyof,26,26f
anomalousoriginoftheleftcoronaryarteryfrom,865,866f–867f,870–872
clinicalpresentationof,870–871
diagnosisof,871–872,871f
incidenceof,870
medicalmanagementof,872
outcomesfor,872
pathophysiologyof,870
surgicalmanagementof,872,872f
treatmentof,872
anomalousrightcoronaryarteryfrom,872–873
bandingof,congenitallycorrectedtranspositionand,713–714
echocardiographicquantificationandidentificationofpatternsofflowin,304–305,304f
Pulmonaryvalvarstenosis
interventionaltechniquesfor,257–258
keydiagnosticfeaturesof,787b
pregnancy,1445
Pulmonaryvalvedisease,chronicrheumaticheartdiseaseand,1030
Pulmonaryvalvereplacement,noveltreatmentsfor,278
Pulmonaryvalves
indiagnosticcatheterization,247
implantationof,interventionaltechniquesfor,259–261,260f
incompetenceof,surgicaltreatmentof,649,649f
three-dimensionalechocardiographyof,314t
Pulmonaryvarix,501
Pulmonaryvascularbed,indiagnosticcatheterization,248–249
Pulmonaryvasculardisease
incongenitalheartdisease,1381
inunrepairedcongenitalheartdisease,1381–1383,1383f
Pulmonaryvascularremodeling,pulmonaryhypertensionand,207
Pulmonaryvascularresistance
elevated,inchronicmechanicalcirculatorysupport,1213–1214
flowthroughventricularseptaldefectand,566
Pulmonaryvasculature,incardiovasculardrugs,1185
Pulmonaryvasodilatortherapy,forpulmonaryhypertension,206
Pulmonaryvasodilators,selective,inuniventricularheart,1348
Pulmonaryvein
common,atresiaof,490
anatomyof,490,494f
clinicalpresentationandinvestigationof,490
imagingof,490
managementof,490
pathophysiologyof,490
embryologyof,37,38f–39f
Pulmonaryveinstenosis,496–501
anatomyof,496,497f,499f
cardiaccatheterizationin,498–499
catheter-basedinterventions,500