surgicalmanagementof,689–690
LeidenConvention,30
LEOPARDsyndrome,1412
hypertrophiccardiomyopathyand,1147
Leukomalacia,periventricular,incongenitalbraindisease,1396–1397
Levocardia,917–918
Levosimendan,foracutecirculatoryfailure,1184t
Liddlesyndrome,hypertensionin,1137
Lidocaine,foratrialtachyarrhythmias,139t
Ligation,ofpulmonaryartery,1280
Limb-girdlemusculardystrophy,cardiacinvolvementin,1103
Linearregression,414
Lipidprofile,inKawasakisyndrome,994
Lipomas,974–975
Literature,criticalappraisalof,403–422
ofharmstudies,420–421
levelsofevidenceand,419,419t
measurementanddescriptionofdata,409–410
pediatriccardiovasculardata,403–409
ofprognosisstudies,420
studydesignand,415–419
oftherapyresultsstudies,420
Liverdisease,Fontan-associated,1331–1334,1331f
clinicalimplications,1335
futuredirections,1335–1336
lymphaticinsufficiency,1332,1333f
neurocognitiveoutcomes,1335
peripheralvasculardisease,1334
plasticbronchitis,1332–1333,1333f–1334f,1333t
protein-losingenteropathy,1333–1334
psychologicalhealth,1335
qualityoflife,1335
Liverphosphorylasedeficiency,cardiacinvolvementin,1089
Localarterialstiffness,1362–1364,1362t,1363f–1364f
Localcontrol,ofcirculation,1357
Loefflerendocarditis,restrictivecardiomyopathyand,1159
Loeys-Dietzsyndrome,cardiacinvolvementin,1078–1079,1079t,1079b,1101,
1101f
LongQTsyndrome(LQTS),351–353,353f
1(KCNQI),353
2(KCNH2),353
3(SCN5A),353
exercisetestingin,401
neonatal,353
pacingfor,366
treatmentof,353–354
LongQT1(KCNQI),353
LongQT2(KCNH2),353
LongQT3(SCN5A),353
Longitudinalanalysis,415
Long-standingandseverehypoxemia,consequencesof,1524–1525,1525f,
1525t
Long-standingvolumeandpressureoverload,adverseeffectsof,1525
Long-termmechanicalcirculatorysupport
currentdevicesfor,1208–1210
useof,1205
Low-andmiddle-incomecountries,pediatriccardiaccarein,1519–1533
congenitalheartdiseasein,patientprofileof,1523–1528
infectionsin,1526–1528,1527t
latepresentationof,1523–1525
undernutritionanditsimpacton,1525–1526,1526f
healthsystemchallengesin,1521–1523,1521b
acquiredheartdisease,1522–1523
congenitalheartdisease,1521–1522,1522t
inresourcelimitedenvironments,delivering,1528–1532
continuingmedicaleducationandtraininginitiativesin,1532
establishingandsustainingpediatricheartprogramsin,1530–1531,1530f,1531t
generalprinciplesof,1526f,1528–1530,1529t
qualityimprovementinitiativesforprogramsin,1532
trainingprogramsin,1531–1532
intouniversalhealthcaremodels,integrating,1531
Lowbirthweight
definitionof,190b
nutritionand,1500
systemicarterialdysfunctionand,1371
Lowcardiacoutput,inmodifiedFontanprocedure,1303–1304,1304t
Low-reninhypertension,1136–1137,1136t
LQTS,LongQTsyndrome
Luminalmyofibroblasticproliferation,980
Lungbiopsy,forpulmonaryhypertension,1388
Lungdisease,restrictive,inFontancirculation,1322–1323
Lunginjury,preterm,pulmonaryhypertensionand,207
Lungtransplantation,hearttransplantationwith,1238–1239
Lungs
developmentof,fetalhemodynamicsand,122,122f–123f
flowofbloodto,fetal,94–95,94f
asserviceorgan,381–382,382f
Lupuserythematosus,neonatal,othermanifestationsof,143
LVoutflowtractcine,320t–321t
LVADsupport,BiVADversus,1210
Lymphaticdrainageabnormalities,noveltreatmentsfor,1351
Lymphaticinsufficiency
inFontancirculation,1333t
inFontan-associatedliverdisease,1332,1333f