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Andersons pediatric cardiology 2357

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echocardiographyin,1151–1152,1152f–1153f
electrocardiographyin,1150,1151f
ambulatory,1150

epidemiologyof,1145
etiologyof,1147–1149,1148t
adenosinemonophosphate-activatedproteinkinasemutationsand,1148
Anderson-Fabrydiseaseand,1149
Danondiseaseand,1147–1148
Friedreichataxiaand,1148–1149
LEOPARDsyndromeand,1147
mitochondrialcardiomyopathiesand,1148
Noonansyndromeand,1147
Pompediseaseand,1149
sarcomericproteindiseaseand,1147

magneticresonanceimagingin,1152,1154f
managementof,1153–1155
fornonobstructivedisease,1154
topreventsuddencardiacdeath,1154–1155
forsymptomscausedbyobstructionofleftventricularoutflowtract,1154

pacingfor,366
pathologyof,1149,1149f
pathophysiologyof,1149–1150

Hyperventilation,terminal,384
Hypoplasticbranchpulmonaryarteries,indiagnosticcatheterization,248,248f
Hypoplasticleftheartsyndrome(HLHS),132
established,withintactorhighlyrestrictiveatrialseptum,154–155
patientselectionfor,155,155f


postnataloutcomeandmanagementof,155
technicalaspectsof,155,155f

evolving,severemidgestationaorticstenosiswith,149–153,150f
patientselectionfor,150,151f
postnataloutcomeandmanagementof,152–153,152f–153f
technicalaspectsof,150–152,151f–152f

noveltreatmentsfor,276–277,277f
inuniventricularhearts,1248–1249,1248f–1250f

Hypoplasticrightheartsyndrome,evolving,pulmonaryatresiawithintact
ventricularseptumand,153–154
patientselectionfor,153–154,154f


postnataloutcomeandmanagementof,154
technicalaspectsof,154

Hypoplasticrightventricle,indiagnosticcatheterization,246
Hypoplasticventricularcavities,804–806,805f–807f
Hypotension
braininjuryand,192–194,194f
inprematurity,200–204
etiologyof,200,201t
therapeuticapproachto,201–204,202f–203f,202t–203t

Hypotheticalpatient,medicalsummaryfor,1488,1489b
Hypothyroidism
cardiacinvolvementin,1096

pericarditisand,1069

Hypovolemia,inprematurity,201
Hypoxemia
long-standingandsevere,consequencesof,1524–1525,1525f,1525t
unanticipated,1268–1270,1268f,1269t

Hypoxia,humanfetalcirculatoryadaptationto,117–118,119f
I
I-celldisease,cardiacinvolvementin,1092
Iduronatesulfatasedeficiency,cardiacinvolvementin,1090–1091
α-L-iduronidasedeficiency,cardiacinvolvementin,1089–1090
Iloprost,forpulmonaryhypertension,1389
Immunesystem,extracardiacanomaliesof,453–454
Immunoglobulin,foratrialtachyarrhythmias,139t
Immunologicabnormalities,inFontancirculation,1330–1331
Immunomodulatoryagents,formyocarditis,1177
Immunosuppression,1437


forcardiactransplantation,1229,1230f

Immunosuppressivetherapy,formyocarditis,1177



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