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Andersons pediatric cardiology 2354

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morphogenesisof,1258–1259,1259f
philosophicalconsiderationswith,1245–1246,1246f–1247f
pulmonaryatresiawithintactventricularseptumin,1249–1250,1250f–1251f
straddlingatrioventricularvalvesin,1254–1256,1255f–1258f
unbalancedatrioventricularseptaldefectin,1256–1257

physiologicprinciplestomaximizeoutcomein,1261–1270
birth,physiologyimmediatelyafter,1261–1264
clinicalpresentationof,1261–1262
fetalandtransitionalcirculation,1262–1264
clarificationsandproposedchangesto,1264–1266
parallelcirculationin,1264–1265,1264f
pulmonaryandsystemicbloodflow,balancing,1264f
pulmonaryovercirculationin,1264f
single-ventriclephysiologyin,1265–1266
medicalmanagementof,1261
stagedreconstructionin
guidingprinciplesof,1261,1262b
physiologiceffectsof,1264f,1266t–1267t
serialphysiologicdataduring,1267t,1268
strategiesandphysiologicgoalsof,optimaloutcomeand,1261,1262t,1263f
superiorcavopulmonaryconnectionin,1266–1267,1266f–1267f
surgicalmanagementof,1261
totalcavopulmonaryconnection(Fontanprocedure)in,1268
unanticipatedhypoxemiain,1268–1270,1268f,1269t
venovenouscollateralsin,1269–1270,1270f–1271f

Furosemide
forhypertension,1140t
forsystemichypertension,inprematureinfants,208f



G
Gadolinium-basedcontrastagent,328
Galactosialidosis,cardiacinvolvementin,1093
α-GalactosidaseAdeficiency,cardiacinvolvementin,1094
Galloprhythm,inKawasakidisease,982
Gangliosidoses,cardiacinvolvementin,1094–1095
Gastroesophagealreflux,oralintakeand,1501
Gastrointestinalcare,forprematurity,211
Gastrointestinalsystem,extracardiacanomaliesof,453
Gastrostomytubefeeding,1500
Gastrulation,33,34f
Gata4
cardiacdevelopmentand,50–51
mutationsof,54–55,55f

Gaucherdisease,cardiacinvolvementin,1093–1094
Geneticfactors
incongenitalheartdisease,49–50
prevalenceofcongenitalheartdiseaseand,177–178,178t
regulatingcardiacformation,50

Genetictesting,forpulmonaryhypertension,1388
Genetics,ofanomaliesofaorticarch,883–886
Genitourinarysystem,extracardiacanomaliesof,454
Genome-wideassociationstudies,incongenitalcardiacdisease,56–57
Genotypescreening,amongfirst-degreerelatives,1539–1540,1540t
Genotype-stratifiedpharmacokineticstudies,1430
Gentamicin
forbloodculture-negativeendocarditis,1054t



forinfectiveendocarditis,1053t

Gerbodedefect,530–531
GermanHeartInstituteMyocarditisRegistryforChildren,1511t–1514t
Giantaneurysms,inKawasakisyndrome,994–995
Gigantism,pituitary,cardiacinvolvementin,1096
Glenncirculation,1265–1266
Glennshunt,bidirectional,forEbsteinmalformation,598–599
Globaloutreach,ethicalissuesin,1478–1479
Globaltelemedicine,1558
α-1,4-Glucan-6-glucosyltransferasedeficiency,cardiacinvolvementin,1089
Glucose,controlof,incardiopulmonarybypass,232
Glucose-6-phosphatasedeficiency,cardiacinvolvementin,1087
Glucose-6-phosphatasetranslocasedeficiency,cardiacinvolvementin,1087
α-1-4-Glucosidasedeficiency,cardiacinvolvementin,1087–1088,1088f
Glucosylceramidosis,cardiacinvolvementin,1093–1094
Glutaraldehydecross-linkedcollagen,inhemostasis,1289
Glutaraldehyde-treatedbovinepericardium,220
Glycogenstoragediseases,cardiacinvolvementin,1087–1089
Glycoproteindegradationdisorders,cardiacinvolvementin,1092–1093
Goldenharsyndrome,1418–1419,1418t
Gordonsyndrome,hypertensionin,1137
Gore-Texsuture,220
Gradientechoimaging,321–322
Greatarteries
morphologyof,6,8f
transpositionof,pulmonaryhypertensionand,122


Greatarteryflow,320t–321t



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