U
Ubiquitinproteasomesystem,70
Udenafil,forpulmonaryhypertension,1390
UDP-glucuronosyltransferases,1434–1435
UGT1A1,1434–1435
UGT1A6,1434–1435
UGT2B7,1434–1435
Uhlmalformation,589–590,603–605,605f
Ultrafiltration,incardiopulmonarybypass,232
Ultrasound
artifactsaffectingimagesof,283
ofcentralnervoussystem,inFontanpathway,1291
imageproductionand,282
imagequalityand,283
physicalpropertiesof,281–282
secondharmonicimaging,282–283
spatialresolutionand,283
temporalresolutionand,283
Umbilicalarterialcatheters,1499
Umbilicalartery,pulse-waveDoppler,129,129f
Umbilicalcord,flowin,fetal,90–91,91f
Umbilicalveins,457
pulse-waveDopplerof,130,131f
Unanticipatedhypoxemia,1268–1270,1268f,1269t
Unbalancedatrioventricularseptaldefect,inuniventricularhearts,1256–1257
Undernutrition,oncongenitalheartdisease,1525–1526,1526f
Unfoldedproteinresponse,69
Univentricularcirculation,functionally,cardiopulmonaryinteractionsin,1183
Univentricularheart,3,6,463–464,1317–1351
Fontancirculationin,Fontancirculation
functionally,anatomicconsiderationsin,1245–1259
atrioventricularvalvaratresiain,1250–1253,1251f–1252f
complexdouble-outletventriclein,1257–1258
double-inletventriclein,1253–1254,1253f–1254f
hypoplasticleftheartsyndromein,1248–1249,1248f–1250f
morphogenesisof,1258–1259,1259f
philosophicalconsiderationswith,1245–1246,1246f–1247f
pulmonaryatresiawithintactventricularseptumin,1249–1250,1250f–1251f
straddlingatrioventricularvalvesin,1254–1256,1255f–1258f
unbalancedatrioventricularseptaldefectin,1256–1257
functionally,physiologicprinciplestomaximizeoutcomein,1261–1270
birth,physiologyimmediatelyafter,1261–1264
clinicalpresentationof,1261–1262
fetalandtransitionalcirculation,1262–1264
clarificationsandproposedchangesto,1264–1266
parallelcirculationin,1264–1265,1264f
pulmonaryandsystemicbloodflow,balancing,1264f
pulmonaryovercirculationin,1264f
single-ventriclephysiologyin,1265–1266
medicalmanagementof,1261
stagedreconstructionin
guidingprinciplesof,1261,1262b
physiologiceffectsof,1264f,1266t–1267t
serialphysiologicdataduring,1267t,1268
strategiesandphysiologicgoalsof,optimaloutcomeand,1261,1262t,1263f
superiorcavopulmonaryconnectionin,1266–1267,1266f–1267f
surgicalmanagementof,1261
totalcavopulmonaryconnection(Fontanprocedure)in,1268
unanticipatedhypoxemiain,1268–1270,1268f,1269t
venovenouscollateralsin,1269–1270,1270f–1271f
futuredirectionsin,1348–1351
exerciseprograms,1348–1349,1349f–1350f
implantedventricularassistdevices,1350–1351
lymphaticdrainageabnormalities,noveltreatmentsfor,1351
othermedicaltherapies,1349
practicevariation,networksandregistries,1349–1350
selectivepulmonaryvasodilators,1348
surgicaldesignandcomputationalfluiddynamics,1350
latepredictorsfor,1320,1320f
inpregnancy,1446
Univentricularjunctions,inisomericatrialappendages,448
Universalhealthcaremodels,integratingpediatrichealthcareinto,1531
Unobstructedsystemicandpulmonarybloodflow,1280,1280f
UNOS,1511t–1514t
Unrepairedcongenitalheartdisease,pulmonaryvasculardiseasein,1381–1383,
1383f
Urinarycatheter,inFontanpathway,1289
USNationalRegistryofSuddenDeathinAthletes,1511t–1514t
V
Vaccines,againstrheumaticfever,1002
VACTERLassociation,1417,1418f,1418t
VAD,Ventricularassistdevice
Vagusnerve,anatomyof,17,19f
Validity,ofdata,409–410
Valproicacid,forcarditis,1017t
Valvarheartdisease,intracardiacinterventionsfor,257–263
Valvarpulmonaryatresia,withintactventricularseptum,interventional
techniquesfor,258,258f
Valvarregurgitation,326–327,327f
Valveareas,indiagnosticcatheterization,242
Valvelessconduits,insurgicaltechniques,220–221
Valves,insurgicaltechniques,221–225
homograft,222,222f
mechanical,221–222,221f
pulmonaryautograft,223
repair,225