geneticconsiderationsin,1375
nutritionalissuesin,1372
prenatalgrowthrestrictionand,1371–1372
systemicdiseaseand,1374–1375
vasculopathies,insyndromaldisorders,1373
Systemicarterialstiffness,1365
Systemicarteries,indiagnosticcatheterization,251
Systemiccirculation,1355–1379
arterialfunction,measurementof,1362–1370
arterialimpedance,asventricularafterload,1360–1361
arterialsystemin,1355–1359
futureof,1379
modelingof,1359–1361,1360f
systemicarterialdysfunctionand,1370–1375
ventriculardysfunctionon,1376
ventriculoarterialinteractionand,1375–1379
arterialdysfunctionon,1375–1376
incongenitalandacquiredheartdisease,1377–1379
ventriculoarterialcouplingin,1376–1377,1376f–1377f
Systemicdiseases,withcardiacinvolvement,1087–1113
Systemicexposure,1436–1437
Systemicfactors,prevalenceofcongenitalheartdiseaseand,178
Systemichypertension,1115–1142
adrenocortical,1136
aorticcoarctationand,1135–1136
burnsand,1138
causesof,1127,1128b,1129t
classificationof,1124–1126,1125f–1127f
clinicalfeaturesof,1128–1130,1129t
complicationsof,1128–1130
definitionof,1124–1126
diagnosisof,1130–1131
drug-induced,1138
essential(primary),1131–1132
exercisetestingin,401
inhypercalcemia,1138
ininfants,1131
investigationfor,1132
low-renin,1136–1137,1136t
managementof,1132–1133
marked,1122
medicaltherapyfor,1139–1142
α-adrenoreceptorblockersfor,1140,1140t
β-adrenoreceptorblockersfor,1140,1140t
angiotensin-convertingenzymeinhibitorsfor,1139,1140t
calcium-channelblockersfor,1139,1140t
diureticsfor,1139–1140,1140t
forhypertensivecrisis,1141–1142,1141t
maintenance,1139,1140t
mixedα-andβ-adrenoreceptorblockersfor,1140
vasodilatorsfor,1140–1141,1140t
inneurologicdisorders,1138
obesityand,1124
pheochromocytomaand,1137–1138
prematurityand,207
causesof,207,207t
treatmentof,207,208f
prevalenceof,1127
primaryhyper-reninismand,1135
renal,1133
pathophysiologyof,1133
renovascular,1133–1135
renalparenchymaldiseaseand,1135
screeningfor,1131
whitecoat,1122
Systemichypoperfusion,preservedmyocardialfunctionwith,1179
Systemicleftventricle,inbiventricularcirculation,1378–1379
Systemiclupuserythematosus
cardiacinvolvementin,1110–1111
myocarditisand,1178
Systemicoxygendelivery,assessmentof,inFontanpathway,1276–1277,1276t,
1290
Systemic-pulmonaryshunt,congenitallycorrectedtranspositionand,711
Systemicrightventricle,inbiventricularcirculation,1379
Systemicsclerosis,cardiacinvolvementin,1109
Systemic-to-pulmonaryarterialconnections,unusualformsof,909,910f
Systemic-to-pulmonarycollateralarteries,morphologyof,657,657f–658f
Systemicveins,indiagnosticcatheterization,243–244
Systemicvenousanomalies,450
anomalous,457–474
withanomalousdrainage,464–468
cavalveinsandhepaticveins,474
connectionbutnormaldrainage,461–464
diagnosisof,471–474
cardiacmagneticresonanceimaging,472
catheterangiography,474
computedtomographicangiography,472
salinecontrastechocardiography,472,473f
managementof,474
portosystemicshunts,474
umbilicalandvitellineveins,471
ofcoronarysinus,461–471,461b
ofembryonicvalvesofsystemicvenoussinus,470–471
morphogenesisof,457–461,458f–460f
totallyanomaloussystemicvenousconnectionand,467–468,468f
Systemicvenousflow,echocardiographicquantificationandidentificationof
patternsof,302–303,303f
Systemicvenoussinus,embryonicvalvesof,anomaliesof,470–471
Systemicvenousstenosis,interventionaltechniquesfor,273,273f
Systemicventricleejectionfraction,Fontanfailurewith
preserved,1344
reduced,1343–1344
Systolicfunction,preserved,withabnormalitiesofdiastolicfunction,1179