Toronto.Thisexcellentstudydetailsrangeof
morphology,outcome,andriskfactorsforpoor
outcomefrom1965to1998.Itisthelargestand
mostcomprehensivesingleinstitutionalstudyto
date.Similarstatisticalmethodstothe
CongenitalHeartSurgeonsStudy..
OdimJ,LaksH,PlunkettMD,TungTC.
Successfulmanagementofpatientswith
pulmonaryatresiawithintactventricularseptum
usingathreetiergradingsystemforright
ventricularhypoplasia.AnnThoracSurg.
2006;81:678–684.
LargeseriesfromUniversityofCaliforniaatLos
Angeles,whereeventualoutcomeispredictedby
presentingrightventricularhypoplasia.
Excellentlong-termsurgicaloutcome..
QuailMA,DaubeneyPEF.Pulmonaryatresiawith
intactventricularseptum.GatzoulisMA,Webb
GD,DaubeneyPEF.DiagnosisandManagement
ofAdultCongenitalHeartDisease.3rded.
Elsevier:Philadelphia;2017:503–512.
Verygoodreviewofthediseaseinadultlife
includingoutcome,complications,and
outpatientassessmentandmanagement..
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