AnnotatedReferences
FreedomRM.PulmonaryAtresiaWithIntact
VentricularSeptum.Futura:MountKisco,NY;
1989.
Asuperbmonographofallfacetsofthisdisease.
Althoughtheoutcomedataaredated,thisisan
excellentresourceforthosewishingfurther
insightintothisdisease..
FreedomRM,AndersonRH,PerrinD.The
significanceofventriculo-coronaryarterial
connectionsinthesettingofpulmonaryatresia
withanintactventricularseptum.Cardiol
Young.2005;15:447–468.
Anencyclopedicreviewostensiblyoftheroleof
fistulasinthisconditionbutcontainingawiderangingreviewofhistoricalperspective,
morphology,pathology,fetaldiagnosis,and
outcome..
FreedomRM,JaeggiE,PerrinD,etal.The“wallto-wall”heartinthepatientwithpulmonary
atresiaandintactventricularseptum.Cardiol
Young.2006;16:18–29.
Afurtherin-depthreviewfocusingonthedilated
RVinthiscondition.Adefinitivereview
containinghistoricalperspective,morphology,
fetaldiagnosis,andoutcome..
HanleyFL,SadeRM,BlackstoneEH,etal.
Outcomesinneonatalpulmonaryatresiawith
intactventricularseptum.JThoracCardiovasc
Surg.1993;105:406–427.
AshburnMD,BlackstoneEH,WellsWJ,etal.
Determinantsofmortalityandtypeofrepairin
neonateswithpulmonaryatresiaandintact
ventricularseptum.JThoracCardiovascSurg.
2004;127:1000–1008.
TheearlyandmidtermresultsfromtheCongenital
HeartSurgeonsStudyofpulmonaryatresiawith
intactventricularseptuminNorthAmerica.This
isthelargeststudyofthediseasetodatewith
408patients.Thereisexcellentstatistical
analysis(parametricmodellingoftime-related
death)particularlyofoptimalinitialprocedure
relatingtothesizeofthetricuspidvalve,and
factorsinfluencingachievementofdefinitive
repair..
DaubeneyPEF,SharlandGK,CookAC,etal.
Pulmonaryatresiawithintactventricular
septum:impactoffetalechocardiographyon
incidenceatbirthandpostnataloutcome.
Circulation.1998;98:562–566.
DaubeneyPE,DelanyDJ,AndersonRH,etal.
Pulmonaryatresiawithintactventricular
septum:rangeofmorphologyinapopulationbasedstudy.JAmCollCardiol.2002;39:1670–
1679.
DaubeneyPEF,WangD,DelanyDJ,etal.
Pulmonaryatresiawithintactventricular
septum:predictorsofearlyandmedium-term
outcomeinapopulation-basedstudy.JThorac
CardiovascSurg.2005;130:1071.
Theresultsfromthecollaborativestudyperformed
intheUnitedKingdomandIreland.Thisisthe
largestpopulation-basedstudyofthisdisease
containingall183patientsborninafixed
geographicalareainafixedtimeframe.There
aredetaileddataaboutfetaldiagnosisandits
effects.Therangeofmorphologyisdescribedin
apopulation-basedsetting,whichcanserveasa
referencetoensurefutureinterventionalstudies
reflectthepopulationatlarge.Outcomedataare
givenandriskfactorsinfluencingpooroutcome.
Therewereahighproportionofprimary
catheterinterventionsinthisstudy..
DyamenahalliU,McCrindleBW,McDonaldC,et
al.Pulmonaryatresiawithintactventricular
septum:managementof,andoutcomesfor,a
cohortof210consecutivepatients.Cardiol
Young.2004;14:299–308.
TheresultsfromHospitalforSickChildren,