AmericanschoolheadedbyMariaVictoriadela
Cruz,asplendidladywhobasedherconcepts
verymuchonherunderstandingofcardiac
embryology.Thesystemhadmuchincommon
withtheapproachtakenbyVanPraaghandhis
colleaguesandwasequallyimportantinguiding
furtherinnovations..
EzonDS,GoldbergJF,KyleWB.Atlasof
CongenitalHeartDiseaseNomenclature.Ezon
EducationalServices:Houston;2015.
Thisatlasprovidesa“dictionary”todemonstrate
thesimilaritiesanddifferencesbetweentheVan
PraaghianandtheAndersonianapproachesto
descriptionofthecongenitallymalformedheart.
Itisprofuselyillustratedwithillustrations
preparedbyGemmaPrice,theartistresponsible
fortheillustrationsinthisbook.Theatlas
discussestheanatomicfeaturesofallthemajor
congenitalcardiaclesions..
JacobsML,AndersonRH.Nomenclatureofthe
functionallyuniventricularheart.CardiolYoung.
2006;16(Suppl1):3–8.
Thisreviewshowedhow,bytheadditionofa
simpleadverb,namely“functionally,”itwas
possibletodefuseallthemultipleargumentsthat
continuedtosurroundso-calledheartswith
“singleventricles.”Mostsuchheartshaveone
bigandonesmallventricle.Thekeypointisthat
onlythebigventricleiscapableofsupporting
oneorotherofthecirculations,orinmost
instancesbothcirculations.Hencethe
arrangement,whilenotanatomically
univentricular,iscertainlyfunctionally
univentricular..
ShinebourneEA,MacartneyFJ,AndersonRH.
Sequentialchamberlocalization:thelogical
approachtodiagnosisincongenitalheart
disease.BrHeartJ.1976;38:327–340.
TynanMJ,BeckerAE,MacartneyFJ,etal.
Nomenclatureandclassificationofcongenital
heartdisease.BrHeartJ.1979;41:544–553.
Thesereviewsrepresentedtheinitialstepstakenby
theEuropeanschoolofnomenclaturiststorefine
thesegmentalapproachtodiagnosis.The
Europeansshiftedemphasisfromthesegments
themselves,whilestillrecognizingthe
importanceofsegmentalmorphology,but
pointingoutatthesametimetheneedtoassess
thewaythecomponentsofthesegmentswere
joinedtogether,orinsomeinstancesnotjoined
together..
VanPraaghR.Thesegmentalapproachto
diagnosisincongenitalheartdisease.Bergsma
D.BirthDefectsOriginalArticleSeries.
WilliamsandWilkins:Baltimore;1972:4–23.
TheNationalFoundation–MarchofDimes.vol.
VIII[No.5].
Thischapterinavolumefromaseriesdevotedto
congenitalmalformationsingeneral
summarizedthe“stateofplay”withsegmental
analysisfollowingthetwoarticlesdiscussed
above.Thesegmentalapproach,withits
shorthandnotations,haschangedlittlesincethis
workwaspublished..
VanPraaghR,DavidI,WrightGB,VanPraaghS.
LargeRVplussmallLVisnotsingleLV.
Circulation.1980;61:1057–1058.
Thiscrucialconcept,statedinalettertotheEditor,
identifiedacrucialflawintheapproachtaken
bytheEuropeanschoolwhenanalyzingpatients
withallegedly“singleventricles,”or
“univentricularhearts.”TheBostonianspointed
outthatitwasphilosophicallyunsoundtobase
definitionsofagivenstructureononeofits
partsthatwasvariable.Instead,theyestablished
thecrucialprincipleofthe“morphologic
method,”statingthatthestructuresbeidentified
onthebasisoftheirmostconstantcomponents..
VanPraaghR,OngleyPA,SwanHJC.Anatomic
typesofsingleorcommonventricleinman:
morphologicandgeometricaspectsofsixty